Crouzon

September 2019
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Crouzon Syndrome
  • Crouzon syndrome occurs in about one of every 100,000 births, and also varies considerably in severity.
  • What is Crouzon Syndrome?Crouzon Syndrome is a condition resulting from premature fusion of the sutures of the skull and deformity of the skull. Characteristics include:
    1. skull is prematurely fused and unable to grow normally (craniosynostosis)
    2. bulging wide -set eyes due to shallow eye sockets (ocular proptosis)
    3. a small underdeveloped upper jaw (maxilla)
    4. downward slanting eyelids
    5. curved, parrot -like nose
    6. high, narrow, arched palate

    Crouzon Syndrome with Acanthosis Nigricans (AN) is found in an estimated 5-10% of all Crouzon cases.

    What kinds of problems could my child have?

    In addition to the physical characteristics common to Crouzon Syndrome, your child may have the following problems:

    • dental problems due to crowded teeth and a narrow palate
    1. poor vision
    2. ear disease and hearing loss in about 50% of children
    3. difficulty breathing due to small airway
    4. possible fluid on the brain (hydrocephalus)